Cystinosin regulates kidney inflammation through its interaction with galectin-3
Tatiana Lobry, Roy Miller, Nathalie Névo, Céline J. Rocca, Jinzhong Zhang, Sergio Daniel Catz, Fiona Moore, A Bailleux, Ida Chiara Guerrera, Marie-Claire Gübler, Cheung W. Wilson, ROBERT H. K. MAK, Tristan Montier, Corinne Antignac, Stéphanie Cherqui
This study shows cystinosin regulates kidney inflammation by interacting with galectin-3, enhancing its lysosomal degradation and reducing macrophage infiltration in cystinosis.
bioRxiv · Mar 27, 2018 · PreprintMolecular Biology