Dysfunctional Mitochondria in Cardiac Fibers of a Williams-Beuren Syndrome Mouse Model
Noura Abdalla, Ester Tobías-Baraja, Alejandro Gonzalez, Glòria Garrabou, Gustavo Egea, Victoria Campuzano
This study examines mitochondrial dysfunction in a Williams-Beuren Syndrome mouse model, finding altered mitochondrial dynamics and respiratory chain dysfunction in cardiac fibers, similar to human WBS fibroblasts.
International Journal of Molecular Sciences · Jun 13, 2023Peer-reviewedMolecular Biology