Knock-in Kcnh2 Rabbit Model of Long QT Syndrome Type-2, Epilepsy, and Sudden Death
Veronica Singh, Kyle T. Wagner, Laura G. Williams, Justin M. Ryan, Katherine R. Keller, Jonathan D. Mohnkern, Robert S. Gardner, Louis T. Dang, Julie M. Ziobro, Richard J.H. Wojcikiewicz, Nathan R. Tucker, David S. Auerbach
This paper develops a knock-in rabbit model of LQT2 with KCNH2 deletion, showing prolonged QT intervals, seizures, and sudden death similar to human LQT2.
Journal of Translational Medicine · Apr 15, 2025Peer-reviewedPhysiology