Epicardial contributions to fibro-inflammatory signaling in a Pkp2-deficient arrhythmogenic cardiomyopathy model
Daniel D Han, Alan C. Brooks, Cameron D. Baker, Ronald A Dirkx, Deanne M. Mickelsen, Benjamin Fisler, Kavya Phadke, John M. Ashton, Mario Delmar, Eric M. Small
This study shows that Pkp2 deficiency in epicardium-derived cells leads to fibro-inflammatory signaling and contributes to arrhythmogenic cardiomyopathy pathogenesis.
Circulation Heart Failure · Jun 5, 2026Peer-reviewedCell Biology