Molecular BiologybioRxivPreprint
Z-AAT impairs organelle homeostasis and reduces adaptive response to lipids in alpha-1 antitrypsin deficiency models
Sara Gil-Martín, Nerea Matamala, Otto Hagen-Doval…·Beatriz Martínez–Delgado
This study investigates how Z-AAT accumulation in AATD models affects lipid metabolism, mitochondrial function, and organelle homeostasis, revealing impaired adaptive responses to lipid challenges.
DOI 10.64898/2026.08.14.744823