NeuroscienceExperimental NeurologyPeer-reviewed
Wobbly hedgehog syndrome- a progressive neurodegenerative disease
Grayson A. Doss, Daniel Z. Radecki, Arya Kethireddy…·Jayshree Samanta
This paper describes Wobbly hedgehog syndrome as a progressive neurodegenerative disease characterized by demyelination, remyelination, axonal degeneration, and neuronal loss, similar to progressive multiple sclerosis.