Frontotemporal dementia-like disease progression elicited by seeded aggregation and spread of FUS
Sonia Vazquez‐Sanchez, Britt Tilkin, Fátima Gasset-Rosa, Sitao Zhang, Diana Piol, Melissa McAlonis‐Downes, Jonathan W. Artates, Noé Govea-Perez, Yana Verresen, Lin E. Guo, Don W. Cleveland, James Shorter, Sandrine Da Cruz
This study shows that injecting human FUS fibrils into mice with human FUS causes FUS aggregation and FTLD-like disease progression, with prion-like spread and cognitive deficits.
Molecular Neurodegeneration · Jun 11, 2024Peer-reviewedNeuroscience