Frataxin depletion leads to decreased soma size and activation of AMPK metabolic pathway in dorsal root ganglia sensory neurons
Olivier Griso, Deepika Mokkachamy Chellapandi, Amélie Weiss, Ioannis Manolaras, Hélène M. Puccio
This study shows that frataxin depletion in DRG neurons causes reduced soma size and activates the AMPK metabolic pathway, with potential therapeutic implications using ALA.
bioRxiv · Oct 7, 2025 · PreprintMolecular Biology