Establishment of spinocerebellar ataxia type 34 model mice accompanied by early glial activation and degeneration of cerebellar neurons
Yuri Morikawa-Yujiri, Kensuke Motomura, Ayumu Konno, Natsuko HitoraーImamura, Yuki Kurauchi, Satohiro Masuda, Hirokazu Hirai, Hiroshi Katsuki, Takahiro Seki
This study establishes a SCA34 mouse model with early glial activation and cerebellar neuron degeneration, linking microglial activation to motor dysfunction and neurodegeneration.
Journal of Pharmacological Sciences · Apr 24, 2026Peer-reviewedNeuroscience