BiochemistrybioRxiv
LONP1 is required for maturation of a subset of mitochondrial proteins and its loss elicits an integrated stress response
O. Zurita Rendon, E. A. Shoubridge
This study shows that LONP1 is necessary for maturing specific mitochondrial proteins and its absence causes stress response activation and mitochondrial dysfunction.
DOI 10.1128/mcb.00412-17