NeurosciencebioRxivPreprint
TLR4-mediated neuroimmune signalling drives proprioceptive neuron degeneration in Friedreich ataxia
Deepika Mokkachamy Chellapandi, Peio Antoine-Uhart, Federica Pilotto, Hélène M. Puccio
This study identifies TLR4-mediated neuroimmune signaling as a driver of proprioceptive neuron degeneration in Friedreich ataxia and shows that inhibiting TLR4 reduces disease progression.
DOI 10.64898/2026.04.28.721289