B Cell Tolerance and BCR Signaling Dysregulation in NF155-Mediated Autoimmune Nodopathies
Bhaskar Roy, Abeer Obaid, Z Wang, Kristof G. Kovacs, Sarah N. Ohashi, F. Naz Cemre Kalayci, Daniel Joo, Gianvito Masi, Carmina Coppola, Sameeran Das, Amanda L. Hernandez, Lorena Martín-Aguilar, Cinta Lleixà, Richard J. Nowak, Luís Querol, Kevin C. O’Connor
This study identifies elevated polyreactive and autoreactive B cells and impaired BCR signaling in NF155-AIN patients, suggesting distinct immunopathology compared to CIDP.
Proceedings of the National Academy of Sciences · Apr 20, 2026Peer-reviewedNeuroscience