Longitudinal Exploration of Auditory Sensory-Perceptual Processing in CLN3 Disease (Juvenile Neuronal Ceroid Lipofuscinosis (Batten disease)): A High-Density Auditory Evoked Potential (AEP) Study.
Erin K. Bojanek, Eve R. Lang, Heather R. Adams, Jennifer A. Vermilion, Erika Fullwood Augustine, Tufikameni Brima, Shahzoda Nasimjonova, Edward G. Freedman, John J. Foxe
This study uses high-density EEG to examine longitudinal changes in auditory processing in CLN3 disease patients compared to controls, finding age-related amplitude differences in auditory evoked potentials.
BMC Neurology · Aug 21, 2026Peer-reviewedNeuroscience