Collagen VI is a conserved pro-fibrotic signal disrupting muscle regeneration across distinct human myopathies
Laura Muraine, Mona Bensalah, Stephen Gargan, Paul Dowling, Anne Bigot, Valérie Allamand, Jamila Dhiab, Maria Kondili, Sophie Périé, Jean Lacau St Guily, Gillian Sandra Butler-Browne, Vincent Mouly, Kay Ohlendieck, Capucine Trollet, Elisa Négroni
This study identifies collagen VI as a conserved pro-fibrotic factor that impairs muscle regeneration in three distinct human myopathies.
bioRxiv · Oct 17, 2025 · PreprintCell Biology