Sulfite oxidase deficiency causes persulfidation loss and H2S release
Chun-Yu Fu, Joshua B. Kohl, Filip Liebsch, Davide D’Andrea, Max Mai, Anna T. Mellis, Emilia Kouroussis, Tamás Ditrói, José Angel Santamaria-Araujo, Sin Yuin Yeo, Heike Endepols, Michaela Křížková, Viktor Kozich, Uladzimir Barayeu, Takaaki Akaike, , Guenter Schwarz
This study shows that SOX deficiency leads to persulfidation loss and increased H2S release, with thiosulfate accumulation and metabolic rewiring in a mouse model.
bioRxiv · Mar 13, 2024 · PreprintBiochemistry