DHTKD1 and OGDH display in vivo substrate overlap and form a hybrid ketoacid dehydrogenase complex
J. Leandro, T. Dodatko, J. Aten, R. C. Hendrickson, R. Sanchez, C. Yu, R. J. DeVita, S. M. Houten
The paper shows DHTKD1 and OGDH share in vivo substrate overlap and form a hybrid ketoacid dehydrogenase complex, with implications for GA1 therapy.
bioRxiv · May 22, 2019Biochemistry