PhysiologybioRxiv
The mechanism underlying transient weakness in myotonia congenita
M. M. Rich, J. H. Myers, K. Denman…·A. A. Voss
This study identifies plateau potentials caused by Na+ and Ca2+ currents in Becker disease models and shows that inhibiting NaPIC with ranolazine prevents transient weakness.
DOI 10.7554/elife.65691