Abnormal triaging of misfolded proteins by adult neuronal ceroid lipofuscinosis-associated CSPα mutants causes lipofuscin accumulation
Y. Ye, J. Lee, Y. Xu, L. Saidi, M. Xu, K. Zinsmaier
This study identifies two distinct roles of CSP in protein quality control, showing that dysfunction leads to lipofuscin accumulation and neurodegeneration in a Drosophila model.
bioRxiv · Jul 16, 2021 · PreprintCell Biology