BiochemistryiSciencePeer-reviewed
SYSTEMIC FRATAXIN DEFICIENCY CAUSES TISSUE-DEPENDENT IRON HOMEOSTASIS ALTERATIONS: IMPLICATIONS FOR FRIEDREICH ATAXIA
Maria Pazos-Gil, Marta Medina‐Carbonero, Arabela Sanz‐Alcázar…·Jordi Tamarit
This study shows that frataxin deficiency causes tissue-specific iron homeostasis changes in FXNI151F mice, with brain iron overload and cardiac iron deficiency responses.
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