Ermin deficiency as an inside-out model of inflammatory dysmyelination
Amin Ziaei, Marta Garcia‐Miralles, Carola I. Radulescu, Harwin Sidik, Aymeric Silvin, Han‐Gyu Bae, Carine Bonnard, Nur Amirah Binte Mohammad Yusof, Costanza Ferrari Bardile, Liang Juin Tan, Alvin Yu Jin Ng, Sumanty Tohari, Leila Dehghani, Lily Henry, Xin Yi Yeo, , Mahmoud A. Pouladi
This study shows that Ermin deficiency causes myelin abnormalities and inflammation, leading to neurological deficits and increased susceptibility to demyelination, suggesting it as an 'inside-out' model for inflammatory dysmyelination.
Brain Pathology · Mar 13, 2022Peer-reviewedNeuroscience