A pathogenic role for histone H3 copper reductase activity in a yeast model of Friedreich's Ataxia
Oscar A. Campos, Narsis Attar, Chen Cheng, Maria Vogelauer, Nathan V. Mallipeddi, Stefan Schmollinger, Nedas Matulionis, Heather R. Christofk, Sabeeha Merchant, Siavash K. Kurdistani
The paper shows that reducing histone H3-mediated Cu1+ production restores Fe-S cluster deficiencies in yeast, linking chromatin and mitochondrial function to Fe-S cluster homeostasis.
Science Advances · Dec 17, 2021Peer-reviewedMolecular Biology