NeuroscienceBrainPeer-reviewed
Activation of XBP1s attenuates disease severity in models of proteotoxic Charcot-Marie-Tooth type 1B
Thierry Touvier, Francesca A Veneri, Anke Claessens…·Maurizio D’Antonio
This study shows that activating XBP1s reduces disease severity in CMT1B models by mitigating ER stress and mutant protein toxicity in Schwann cells.
15 citations