Perinuclear damage from nuclear envelope deterioration elicits stress responses that contribute to LMNA cardiomyopathy
K. Sikder, E. Phillips, Z. Zhong, N. Wang, J. Saunders, D. Mothy, A. Kossenkov, T. Schneider, Z. Nichtova, G. Csordas, K. B. Margulies, J. C. Choi
This study identifies perinuclear stress responses from nuclear envelope deterioration as contributors to LMNA cardiomyopathy using a mouse model and translatome profiling.
bioRxiv · Feb 14, 2023 · PreprintCell Biology