NeuroscienceBrainPeer-reviewed
Defective cyclophilin A induces TDP-43 proteinopathy: implications for amyotrophic lateral sclerosis and frontotemporal dementia
Laura Pasetto, Maurizio Grassano, Silvia Pozzi…·Valentina Bonetto
This study shows that defective cyclophilin A (PPIA) leads to TDP-43 proteinopathy, contributing to ALS and FTD by disrupting TDP-43 function and causing neurodegeneration.
32 citations