NeuroscienceMolecular MedicinePeer-reviewed
Skeletal myotubes expressing ALS mutant SOD1 induce pathogenic changes, impair mitochondrial axonal transport, and trigger motoneuron death.
Pablo Martínez, Mónica Silva, Sebastián Abarzúa…·Brigitte van Zundert
This study shows that skeletal myotubes with ALS-linked mutant SOD1 release factors that cause motoneuron axonopathy and death.
10 citations