iPSC-derived skeletal muscle spheroids for Duchenne Muscular Dystrophy modeling
Joyce Esposito, Felipe de Souza Leite, Igor Neves Barbosa, Thaís Maria da Mata Martins, Giovanna Gonçalves de Oliveira Olberg, Ziad Al Tanoury, Kayque Alves Telles-Silva, Mayana Cristina da Silva Pardo, Tatiana Jazedje, Raul Hernandes Bortolin, Mário Hiroyuki Hirata, Olivier Pourquié, Mayana Zatz
This study compares 3D skeletal muscle spheroids (iSMS) with 2D cultures for modeling Duchenne Muscular Dystrophy, finding improved PAX7 expression and altered Notch signaling in iSMS.
Skeletal Muscle · May 2, 2026Peer-reviewedCell Biology