NeurosciencebioRxivPreprint
Disarrangement of Endoplasmic reticulum-mitochondria communication impairs Ca2+ homeostasis in FRDA
Laura R. Rodríguez, Pablo Calap-Quintana, Tamara Lapeña-Luzón…·Pilar González‐Cabo
This study shows that frataxin deficiency disrupts ER-mitochondria communication, impairing calcium homeostasis in FRDA models, and that restoring mitochondrial calcium uptake can alleviate some defects.
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