MCUR1-CCDC90B complex is a conserved mitochondrial scaffold regulating metabolic homeostasis
J Verissimo Ferreira, Jennifer Wettmarshausen, Valerie Goh, K Lagerborg, J Watrous, MS Feng, H Delgado de la Herran, S Walia, Y Cheng, A Leimpek, M Gorza, S Braun, R Nilsson, Mohit Jain, Matthias Mann, , F Perocchi
This study identifies the MCUR1-CCDC90B complex as a mitochondrial scaffold regulating metabolic homeostasis, showing its role in amino acid metabolism and linking its deficiency to neurometabolic disease.
bioRxiv · Oct 14, 2025 · PreprintCell Biology