Defective mesenchymal Bmpr1a-mediated BMP signaling causes congenital pulmonary cysts
Yongfeng Luo, Ke Xin Cao, Joanne Chiu, Hui Chen, Hongjun Wang, Matthew Edward Thornton, Brendan H. Grubbs, Martin R.J. Kolb, Michael S. Parmacek, Yuji M. Mishina, Wei Shi
This study identifies defective mesenchymal Bmpr1a-mediated BMP signaling as a cause of congenital pulmonary cysts by disrupting lung branching morphogenesis and airway structure.
eLife · Jun 10, 2024Peer-reviewedDevelopmental Biology