Neuregulin 1 type III reduces severity in a mouse model of Congenital Hypomyelinating Neuropathy
Sophie Belin, Francesca Ornaghi, Ghjuvan’Ghjacumu Shackleford, Jie Wang, Cristina Scapin, Camila Lopez‐Anido, Nicholas J. Silvestri, Neil Robertson, Courtney Williamson, Akihiro Ishii, Carla Taveggia, John P. Svaren, Rashmi Bansal, Markus H. Schwab, Klaus‐Armin Nave, , Lawrence G. Wrabetz
This study shows that increasing neuregulin 1 type III in neurons improves myelination in a mouse model of congenital hypomyelinating neuropathy without relying on Egr2 or typical myelin genes.
bioRxiv · Aug 7, 2018 · PreprintNeuroscience