YBEY is an essential biogenesis factor for mitochondrial ribosomes
Sabrina Summer, Anna Smirnova, Alessandro Gabriele, Ursula Toth, Akinyemi M. Fasemore, Konrad U. Förstner, Lauriane Kühn, Johana Chicher, Philippe Hammann, Goran Mitulović, Nina Entelis, Ivan Tarassov, Walter Rossmanith, Alexandre Smirnov
This study shows that human YBEY is essential for mitochondrial ribosome biogenesis, leading to respiratory deficiency and mitochondrial abnormalities.
Nucleic Acids Research · Feb 26, 2020Peer-reviewedMolecular Biology