A mouse model of CHCHD10 p.R15L familial ALS presents mild, age-related motor neuron degeneration without protein instability or mitochondrial dysfunction
JoonHyung Park, Анна Степанова, Jalia Dash, Nneka Southwell, Dazhi Zhao, Csaba Konràd, Paridhi Taygi, Justin Y. Kwan, Neil A. Shneider, George Z. Mentis, Giovanni Manfredi, Hibiki Kawamata
bioRxiv · Dec 29, 2025 · PreprintNeuroscience