Chlorzoxazone, A BKCa Channel Agonist, Rescues The Pathological Phenotypes Of Williams-Beuren Syndrome In A Preclinical Model
Marion Piquemal, Noura Abdalla, Paula Ortiz‐Romero…·Susanna Pietropaolo
This paper shows that chlorzoxazone, a BKCa channel agonist, improves multiple pathological features in a mouse model of Williams-Beuren syndrome.