BiochemistrybioRxivPreprint
Poly-alanine-tailing is a modifier of neurodegeneration caused by Listerin mutation
Hao‐Chih Hung, Carlos Costas‐Insua, Sarah E. Holbrook…·Claudio A.P. Joazeiro
This study shows that impairing NEMF's poly-alanine-tailing activity in mice interacts with Listerin mutations to cause neurodegeneration, revealing a role for Ala-tailing in proteostasis and neurodegeneration.